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Case Reports 2018
Medical Case Reports
ISSN: 2471-8041
Page 65
May 28-29, 2018
London, UK
8
th
Edition of International Conference on
Clinical and Medical Case Reports
P
entalogy of cantrell consists of an extensive defect of the
thoraco-abdominal wall, which has nearly always a lethal
prognosis. The defect is characterized by the association of
five anomalies: omphalocele, cardiac ectopia, absence of the
distal portion of the sternum, absence of the anterior diaphragm
and absence of the parietal diaphragmatic pericardium. It has
a rare frequency of about 5.5 per 1,000,000 live births. There
is a common association with intra cardiac anomalies such as
ventricular septum defect, tetralogy of fallot and transposition
of great vessels. The pathogenesis remains unclear. Here we
present an imaging findings with antenatal two dimensional
(2D) and three dimensional (3D) ultrasound and fetal magnetic
resonance imaging (MRI) in a 20 weeks of gestation with a
multiple anomalies, based on which the diagnosis of complete
pentalogy of cantrell was givenwith a brief literature. Postmortem
radiography, 3D computed tomography (CT) and clinical autopsy
were performed additionally to enhance the visualization of fetal
anomalies and to confirm the diagnosis. Extensive imaging of
cardiac, thoracic and abdominal malformations by ultrasound
and MRI is complementary for a clear diagnosis and counseling
of the patient.
leuladane2@gmail.comA rare case report of complete expression of pentalogy of
cantrell: from radiology perspective
Antenatal ultrasound, fetal echo and fetal MRI, post
termination radiography and 3D CT findings with a clinical
autopsy correlation:
Med Case Rep. 2018, Volume 4
DOI: 10.21767/2471-8084-C1-003
Leul Adane, Alemayehu Bedane, Fitehanegest Tefera
and
Satyasai Panda
Saint Paul Hospital Millennium Medical College, Ethiopia